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Madelung’s disease in a patient with chronic renal insufficiency: a case report and review of
Beata Bergler-Czop
简介
【 文献重点摘要 】
Madelung’s disease (benign symmetric lipomatosis, Launois-Bensaude syndrome) was described for the first time in the middle of the 19th century. This disorder concerns mainly men between 30 and 60 years of age. Patients often suffer from coexisting ailments, such as hepatic function disorders, polyneuropathy, diabetes, gynecomastia, hyperuricemia and deviations of lipid management parameters. Treatment of benign symmetric lipomatosis consists mainly in fat tissue sucking or injection lipolysis. Patients often have to wear special clothes correcting the deformed figure. We are presenting a case of a female patient with diagnosed Madelung’s disease, without alcohol abuse. Such abuse is reported in 90% of patients with this disease. Nevertheless, the patient has other typical (and described in the literature) hepatic and pancreatic function impairments, but also glomerular nephritis, which very rarely co-exists with benign symmetric lipomatosis.
Keywords
Madelung’s disease, lipomatosis, treatment
马德隆病(良性对称性脂肪瘤病，劳诺瓦-本苏德综合征)于19世纪中叶首次被描述。这种疾病主要影响30到60岁的男性。患者常伴有肝功能紊乱、多发性神经病、糖尿病、女性乳房发育症、高尿酸血症和脂质管理参数偏差等并存疾病。良性对称性脂肪瘤的治疗主要以脂肪组织吸入或注射脂肪溶解为主。病人经常不得不穿着特殊的衣服来矫正畸形的身材。我们报告的是一例女性患者，诊断为马德隆氏病，没有酗酒。据报道，这种虐待在90%的这种疾病患者中发生。然而，患者有其他典型的(文献中描述的)肝和胰腺功能损害，但也有肾小球肾炎，这很少与良性对称性脂肪瘤共存。
关键词
马德隆病，脂肪瘤病，治疗
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